3-hydroxyisovaleryl-CoA

362,296 routes · scope human · up to 3 steps · built 5 October 2026 · Reactions · API

555 compounds within 3 steps: 2 in 1, 108 in 2, 445 in 3

One step

CHEBI:1146900Reach from here →
1. (3-Hydroxyisovalerylcoa->3-Hydroxyisovalerylcarnitine)
Catalysed by CPT1A, CPT1BcytosolOne of 2 routes
3-hydroxyisovaleric acidReach from here →
1. Formation of 3-Hydroxy-Isovalerate
No catalyst recordedmitochondrial matrix

Two steps

(S)-carnitineReach from here →
1. (3-Hydroxyisovalerylcoa->3-Hydroxyisovalerylcarnitine)
2. Carnitine O-Palmitoyltransferase
Catalysed by CPT1A, CPT1B, CPT1CcytosolOne of 244 routes
(7Z)-octadecenoyl-CoAReach from here →
1. (3-Hydroxyisovalerylcoa->3-Hydroxyisovalerylcarnitine)
2. carnitine O-palmitoyltransferase ((7Z)-octadecenoyl-CoA)
Catalysed by CPT1A, CPT1B, CPT1CcytosolOne of 3 routes

CHEBI:15345

Reach from here →

Catalysed by CPT1A, CPT1B, AACScytosolOne of 2 routes

cholineReach from here →

Catalysed by CPT1A, CPT1B, CHATcytosol, nucleus

CHEBI:15380Reach from here →

Catalysed by CPT1A, CPT1B, ALAS1, CPNE7cytosol, mitochondrial matrixOne of 8 routes

CHEBI:15477Reach from here →

Catalysed by CPT1A, CPT1B, GLYAT, GLYATL2 and 1 morecytosol, mitochondrial matrixOne of 2 routes

2-methylcrotonoyl-CoAReach from here →

Catalysed by CPT1A, CPT1BcytosolOne of 2 routes

isobutyryl-CoAReach from here →

Catalysed by CPT1A, CPT1B, HADHA, ACAA2 and 1 morecytosol, mitochondrial matrixOne of 3 routes

3-methylbut-2-enoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, GLYATcytosol, mitochondrial matrix

isovaleryl-CoAReach from here →

Catalysed by CPT1A, CPT1B, GLYAT, GLYATL2 and 1 morecytosol, mitochondrial matrixOne of 3 routes

arachidonoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 11 routes

CHEBI:15519Reach from here →

Catalysed by CPT1A, CPT1B, ACAA1, SCP2 and 1 morecytosol, peroxisomeOne of 2 routes

palmitoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 11 routes

oleoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, CPT1CcytosolOne of 11 routes

phenylacetyl-CoAReach from here →

Catalysed by CPT1A, CPT1BcytosolOne of 3 routes

propionyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, ACSS3, ACSS2 and 1 morecytosolOne of 43 routes

CHEBI:15650Reach from here →

Catalysed by CPT1A, CPT1B, ZDHHC11B, NAA10 and 30 morecytosolOne of 2 routes

CHEBI:15727Reach from here →

Catalysed by CPT1A, CPT1B, NAA10cytosol

CHEBI:15746Reach from here →

Catalysed by CPT1A, CPT1B, SAT1, SAT2cytosolOne of 2 routes

11-cis-retinolReach from here →

Catalysed by CPT1A, CPT1B, DGAT1, LRAT and 3 morecytosol

oxaloacetateReach from here →

Catalysed by CPT1A, CPT1B, ACLYcytosol

anilineReach from here →

Catalysed by CPT1A, CPT1B, NAT2, NAT1cytosol

CHEBI:17312Reach from here →

Catalysed by CPT1A, CPT1BcytosolOne of 2 routes

L-cysteineReach from here →

Catalysed by CPT1A, CPT1B, NAGScytosol, mitochondrial matrix

(7Z,10Z,13Z)-hexadecatrienoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, HADHA, ACADVL and 1 morecytosol, mitochondrial matrix

CHEBI:17927Reach from here →

Catalysed by CPT1A, CPT1Bcytosol

(5Z)-dodecenoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, HADHA, ACAA2 and 1 morecytosol, mitochondrial matrixOne of 2 routes

(11Z)-docosenoyl-CoA(4-)Reach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 5 routes

(7Z)-tetradecenoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 8 routes

(4Z,7Z,10Z,13Z)-hexadecatetraenoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, HADHA, ACADVL and 1 morecytosol, mitochondrial matrixOne of 3 routes

(7Z,10Z)-hexadecadienoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, HADHA, ACADVL and 1 morecytosol, mitochondrial matrix

(4Z,7Z)-decadienoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, ECHS1, ACAA2 and 1 morecytosol, mitochondrial matrixOne of 2 routes

(5Z)-octenoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, ECHS1, ACAA2 and 1 morecytosol, mitochondrial matrixOne of 2 routes

CHEBI:27540Reach from here →

Catalysed by CPT1A, CPT1B, ACSM4, ACSM1 and 4 morecytosolOne of 6 routes

elaidic acidReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 5 routes

CHEBI:28701Reach from here →

Catalysed by CPT1A, CPT1B, ACAA1, SCP2 and 1 morecytosol, peroxisomeOne of 7 routes

taurineReach from here →

Catalysed by CPT1A, CPT1B, BAATcytosolOne of 2 routes

glycineReach from here →

Catalysed by CPT1A, CPT1B, GLYAT, GLYATL2 and 1 morecytosol, mitochondrial matrixOne of 10 routes

(R)-methylmalonyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, ALDH6A1cytosol, mitochondrial matrixOne of 2 routes

(S)-methylmalonyl-CoAReach from here →

Catalysed by CPT1A, CPT1Bcytosol, mitochondrial matrix

3'-dephospho-CoAReach from here →

Catalysed by CPT1A, CPT1B, ACP2cytosol, lysosomeOne of 2 routes

(2E)-dodecenoyl-CoAReach from here →

Catalysed by CPT1A, CPT1Bcytosol, mitochondrial matrixOne of 3 routes

4,8,12-trimethyltridecanoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, ACAA1, MYO5Bcytosol, peroxisomeOne of 2 routes

(6Z,9Z,12Z)-octadecatrienoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 7 routes

butanoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, ACSM4, ACSM1 and 4 morecytosolOne of 9 routes

dodecanoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 9 routes

glutaryl-CoAReach from here →

Catalysed by CPT1A, CPT1B, CPT1CcytosolOne of 2 routes

eicosanoyl-CoAReach from here →

Catalysed by CPT1A, CPT1B, SLC27A2, ACSL4 and 6 morecytosolOne of 12 routes