beta-alanine

362,296 routes · scope human · up to 3 steps · built 5 October 2026 · Reactions · API

516 compounds within 3 steps: 9 in 1, 87 in 2, 420 in 3

One step

CHEBI:15727Reach from here →
1. L-histidine:beta-alanine ligase (ADP-forming)
Catalysed by CARNS1cytosol
3-oxopropanoic acidReach from here →
1. beta-alanine:2-oxoglutarate aminotransferase
Catalysed by ABATmitochondrial matrix
chlorine(.)Reach from here →
1. transport of beta-alanine and chloride (cytosol to extracellular)
Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 2 routes
L-aspartateReach from here →
1. L-aspartate + H(+) = beta-alanine + CO2
Catalysed by GADL1, CSAD
3-oxopropanoateReach from here →
1. 3-oxopropanoate + L-alanine = beta-alanine + pyruvate
Catalysed by AGXT2
L-ornithineReach from here →
1. beta-alanine + L-arginine = 3-guanidinopropanoate + L-ornithine
Catalysed by GATM
carnosineReach from here →
1. beta-alanine + L-histidine + ATP = carnosine + ADP + phosphate + H(+)
Catalysed by CARNS1
3-guanidinopropanoateReach from here →
1. beta-alanine + L-arginine = 3-guanidinopropanoate + L-ornithine
Catalysed by GATM
L-alanineReach from here →
1. 3-oxopropanoate + L-alanine = beta-alanine + pyruvate
Catalysed by AGXT2One of 3 routes

Two steps

(S)-carnitineReach from here →
1. transport of beta-alanine and chloride (cytosol to extracellular)
2. Carnitine Transport by Atb0
Catalysed by SLC6A6, SLC6A14extracellular space, cytosol
CHEBI:1146900Reach from here →
1. L-histidine:beta-alanine ligase (ADP-forming)
2. N-alpha-acetyltransferase 10, NatA catalytic subunit (acetylcarnosine)
Catalysed by CARNS1, NAA10cytosolOne of 3 routes
N(omega)-methyl-L-arginineReach from here →

Catalysed by AGXT2

D-histidineReach from here →

Catalysed by GATM, SLC25A2inner side of the membrane, outer side of the membraneOne of 2 routes

L-homoarginineReach from here →

Catalysed by GATM, SLC25A2inner side of the membrane, outer side of the membraneOne of 2 routes

cholineReach from here →

Catalysed by SLC6A6, SLC6A14, SLC5A7extracellular space, cytosol

pyruvateReach from here →

Catalysed by AGXT2mitochondrial matrixOne of 14 routes

CHEBI:15570Reach from here →

Catalysed by AGXT2cytosol

L-leucineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 12 routes

CHEBI:15699Reach from here →

Catalysed by AGXT2, SLC7A5extracellular space, cytosolOne of 5 routes

N-carbamoyl-L-aspartic acidReach from here →

Catalysed by GADL1, CSAD, CADcytosol

CHEBI:15971Reach from here →

Catalysed by CARNS1, CNDP1, CNDP2cytosolOne of 8 routes

sulfateReach from here →

Catalysed by SLC6A6, SLC6A14, SLC26A6extracellular space, cytosolOne of 3 routes

ureaReach from here →

Catalysed by GATM, AGMAT

L-cystineReach from here →

Catalysed by AGXT2, SLC7A9, SLC3A1extracellular space, cytosolOne of 3 routes

(R)-3-aminoisobutyric acidReach from here →

Catalysed by AGXT2mitochondrial matrix

L-citrullineReach from here →

Catalysed by AGXT2, SLC7A6extracellular space, cytosolOne of 11 routes

iodideReach from here →

Catalysed by SLC6A6, SLC6A14, SLC26A4extracellular space, cytosol

L-valineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 12 routes

oxaloacetateReach from here →

Catalysed by GADL1, CSAD, GOT2mitochondrial matrixOne of 5 routes

L-arginineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 12 routes

protein polypeptide chainReach from here →

Catalysed by AGXT2cytosolOne of 2 routes

N(2)-acetyl-L-ornithineReach from here →

Catalysed by GATM, ACY1cytosol

CHEBI:16633Reach from here →

Catalysed by AGXT2, SCLYcytosol

CHEBI:16857Reach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 7 routes

N-acetyl-L-aspartateReach from here →

Catalysed by GADL1, CSAD, NAT8Lmitochondrial matrixOne of 2 routes

oxalic acidReach from here →

Catalysed by SLC6A6, SLC6A14, SLC26A6extracellular space, cytosol

L-isoleucineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 7 routes

CHEBI:17203Reach from here →

Catalysed by SLC6A6, SLC6A14, CLTRN, SLC6A20extracellular space, cytosolOne of 8 routes

L-glutamic 5-semialdehydeReach from here →

Catalysed by GATM, OATmitochondrial matrix

AH2Reach from here →

Catalysed by AGXT2, MOCOS

L-cysteineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 15 routes

Ala-tRNA(Ala)Reach from here →

Catalysed by AGXT2, AARS1cytosol

glycine betaineReach from here →

Catalysed by SLC6A6, SLC6A14, SLC6A12extracellular space, cytosolOne of 3 routes

CHEBI:17895Reach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 8 routes

CHEBI:18019Reach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 7 routes

L-glutamineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 11 routes

CHEBI:18095Reach from here →

Catalysed by SLC6A6, SLC6A14, CLTRN, SLC6A20extracellular space, cytosolOne of 2 routes

N-carbamoyl-beta-alanineReach from here →

Catalysed by SLC6A6, SLC6A14extracellular space, cytosolOne of 2 routes

2-aminoisobutanoateReach from here →

Catalysed by AGXT2, SLC7A10inner side of the membrane, outer side of the membraneOne of 2 routes

N(omega),N('omega)-dimethyl-L-arginineReach from here →

Catalysed by AGXT2