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Proteins/UNIPROT:P80404
Catalyzes the conversion of gamma-aminobutyrate and L-beta-aminoisobutyrate to succinate semialdehyde and methylmalonate semialdehyde, respectively. Can also convert delta-aminovalerate and beta-alanine (By similarity)..
Function from UniProtKB (P80404), read 2026-09-23. CC BY 4.0.
Curated compounds routed: 1 · substrate of
1 compound
1 compound.
0 reported routes1 assembled route
2 rows
318 statements
318 statements · 9 reference databases · Subject: ABAT · Sources: Bgee, gene ontology, Hetionet, Human Protein Atlas, Human-GEM, Reactome, Rhea, UniProt, WikiPathways · Rows fetched: 300
7 reactions
2-methyl-3-oxopropanoic acid+L-glutamate(1-)2-oxoglutarate(2-)+(R)-3-aminoisobutyric acid
Reaction pageReversibleBalancedEC 2.6.1.22, 2.6.1.40mitochondrial matrix
Human-GEM MAR03792CC BY 4.0Reference data
3-oxopropanoic acid+L-glutamate(1-)2-oxoglutarate(2-)+beta-alanine
Catalysed by ABAT
8 names
Resolves to: ABAT
Human-GEM MAR04330CC BY 4.0Reference data
4-aminobutanoate+2-oxoglutarate(2-)L-glutamate(1-)+succinic semialdehyde
Catalysed by ABAT
Reaction pageReversibleBalancedEC 2.6.1.19mitochondrial matrix
Human-GEM MAR04693CC BY 4.0Reference data
2-methyl-3-oxopropanoic acid+L-glutamate(1-)2-oxoglutarate(2-)+(S)-3-amino-2-methylpropanoate
Catalysed by ABAT
Reaction pageReversibleBalancedEC 2.6.1.22mitochondrial matrix
Human-GEM MAR08088CC BY 4.0Reference data
(S)-3-amino-2-methylpropanoate(S)-3-amino-2-methylpropanoate
Transported by ABAT
Reaction pageLeft to rightBalancedmitochondrial matrix, cytosol
Human-GEM MAR08089CC BY 4.0Reference data
(S)-3-amino-2-methylpropanoate+2-oxoglutarate(2-)2-methyl-3-oxopropanoate+L-glutamate(1-)
Catalysed by ABAT
Reaction pageLeft to rightBalanced
Rhea RHEA:13993CC BY 4.0Reference data
4-aminobutanoate+2-oxoglutarate(2-)succinate semialdehyde+L-glutamate(1-)
Catalysed by ABAT
Reaction pageLeft to rightBalanced
Rhea RHEA:23352CC BY 4.0Reference data