(S)-methylmalonyl-CoA

1. (S)-methylmalonyl-CoA hydrolase
2. Production of Sebacoylcarnitine

Catalysed by CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 4 routes

1. (S)-methylmalonyl-CoA hydrolase
2. Production of Suberylcarnitine

Catalysed by CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 4 routes

1. (S)-methylmalonyl-CoA hydrolase
2. Activation of adipic acid for Formation of Adipoyl Carnitine

No catalyst recordedmitochondrial matrix, cytosolOne of 4 routes

1. (S)-methylmalonyl-CoA hydrolase
2. long-chain-fatty-acid-CoA ligase ((4Z,7Z,10Z,13Z,16Z)-DPA)

Catalysed by SLC27A2, ACSL4, ACSL3, ACSL1 and 4 moremitochondrial matrix, cytosolOne of 7 routes

1. (S)-methylmalonyl-CoA hydrolase
2. long-chain-fatty-acid-CoA ligase ((11Z,14Z)-eicosadienoic acid)

Catalysed by SLC27A2, ACSL4, ACSL3, ACSL1 and 4 moremitochondrial matrix, cytosolOne of 5 routes

1. (S)-methylmalonyl-CoA hydrolase
2. Production of 3-Hydroxyoctadecenoylcarnitinec

Catalysed by CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosol

1. (S)-methylmalonyl-CoA hydrolase
2. long-chain-fatty-acid-CoA ligase ((13Z)-eicosenoic acid)

Catalysed by SLC27A2, ACSL4, ACSL3, ACSL1 and 4 moremitochondrial matrix, cytosolOne of 5 routes

1. (S)-methylmalonyl-CoA hydrolase
2. Carnitine Dimethyl Nonanoyl Transferase, Revsible, Peroxisomal

Catalysed by CRAT, CROTmitochondrial matrix, peroxisomeOne of 3 routes

1. (S)-methylmalonyl-CoA hydrolase
2. Fatty Acid Beta Oxidation (C16Dc->C14Dc), Peroxisomal

Catalysed by ACAA1, HSD17B4, EHHADH, ACOX1mitochondrial matrix, peroxisome

1. (S)-methylmalonyl-CoA hydrolase
2. Production of Hexadecanedioylcarnitine

Catalysed by CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 2 routes

1. (S)-methylmalonyl-CoA hydrolase
2. fatty-acid-CoA ligase

Catalysed by SLC27A2mitochondrial matrix, cytosolOne of 2 routes

1. (S)-methylmalonyl-CoA hydrolase
2. medium-chain acyl-CoA ligase (undecylic acid)

Catalysed by ACSM4, ACSM1, ACSM2A, ACSM3 and 2 moremitochondrial matrix, cytosolOne of 3 routes

1. (S)-methylmalonyl-CoA hydrolase
2. long-chain-fatty-acid-CoA ligase (physeteric acid)

Catalysed by SLC27A2, ACSL4, ACSL3, ACSL1 and 4 moremitochondrial matrix, cytosolOne of 8 routes

1. (S)-methylmalonyl-CoA hydrolase
2. Fatty Acid Beta Oxidation (C12:1->C10:1), Mitochondrial

Catalysed by ACADM, ECHS1, ACAA2, HADHmitochondrial matrix

1. (S)-methylmalonyl-CoA hydrolase
2. acetyl-CoA C-acyltransferase (3-oxo-4(R),8-dimethyl-nonanoyl-CoA)

Catalysed by HADHA, ACAA2, HADHBmitochondrial matrix

1. (S)-methylmalonyl-CoA hydrolase
2. long-chain-fatty-acid-CoA ligase (7-palmitoleic acid)

Catalysed by SLC27A2, ACSL4, ACSL3, ACSL1 and 4 moremitochondrial matrix, cytosolOne of 8 routes

1. (S)-methylmalonyl-CoA + H(+) = propanoyl-CoA + CO2
2. propanoyl-CoA + glyoxylate + H2O = 3-methylmalate + CoA + H(+)

Catalysed by ECHDC1, CLYBL

1. (S)-methylmalonyl-CoA hydrolase
2. long-chain-fatty-acid-CoA ligase (tricosanoic acid)

Catalysed by SLC27A2, ACSL4, ACSL3, ACSL1 and 4 moremitochondrial matrix, cytosolOne of 4 routes

1. methylmalonyl-CoA decarboxylase
2. Propanoyl-CoA hydrolase
3. transport of 2-hydroxybutyrate and propanoate (cytosol to extracellular)

Catalysed by MLYCD, ACOT7, SLC16A4, SLC16A5 and 2 morecytosol, extracellular spaceOne of 2 routes

1. (S)-methylmalonyl-CoA hydrolase
2. glycine N-acyltransferase (N-arachidonoylglycine)
3. N(omega)-methyl-L-arginine + glyoxylate = 5-(3-methylguanidino)-2-oxopentanoate + glycine