Mo-molybdopterin
362,296 routes · scope human · up to 3 steps · built 5 October 2026 · Reactions · API
457 compounds within 3 steps: 3 in 1, 56 in 2, 398 in 3
Three steps
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase ((6Z,9Z,12Z,15Z,18Z,21Z)-THA)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 4 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (nervonic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 6 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (ximenic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 4 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (dihomo-gamma-linolenate)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 5 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (omega-3-arachidonic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 5 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (DHA)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 7 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (margaric acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 6 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (9-heptadecylenic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 5 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase ((11Z,14Z,17Z)-eicosatrienoic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 5 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (nonadecylic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 6 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Transport of 11-Octadecenoyl Carnitine into the Mitochondrial Matrix
Catalysed by MOCOS, CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 3 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Activation of dodecanedioic acid
Catalysed by MOCOSmitochondrial matrix, cytosolOne of 4 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Production of Sebacoylcarnitine
Catalysed by MOCOS, CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 4 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Production of Suberylcarnitine
Catalysed by MOCOS, CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 4 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Activation of adipic acid for Formation of Adipoyl Carnitine
Catalysed by MOCOSmitochondrial matrix, cytosolOne of 4 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase ((4Z,7Z,10Z,13Z,16Z)-DPA)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 7 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase ((11Z,14Z)-eicosadienoic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 5 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Production of 3-Hydroxyoctadecenoylcarnitinec
Catalysed by MOCOS, CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosol
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase ((13Z)-eicosenoic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 5 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- D-serine(out) + L-alanine(in) = D-serine(in) + L-alanine(out)
- D-serine = 2-aminoprop-2-enoate + H2O
Catalysed by MOCOS, SLC7A10, SRRinner side of the membrane, outer side of the membrane
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Carnitine Dimethyl Nonanoyl Transferase, Revsible, Peroxisomal
Catalysed by MOCOS, CRAT, CROTmitochondrial matrix, peroxisomeOne of 3 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Fatty Acid Beta Oxidation (C16Dc->C14Dc), Peroxisomal
Catalysed by MOCOS, ACAA1, HSD17B4, EHHADH and 1 moremitochondrial matrix, peroxisome
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Production of Hexadecanedioylcarnitine
Catalysed by MOCOS, CPT1A, CPT1C, CPT1Bmitochondrial matrix, cytosolOne of 2 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- fatty-acid-CoA ligase
Catalysed by MOCOS, SLC27A2mitochondrial matrix, cytosolOne of 2 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- medium-chain acyl-CoA ligase (undecylic acid)
Catalysed by MOCOS, ACSM4, ACSM1, ACSM2A and 3 moremitochondrial matrix, cytosolOne of 3 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- all-trans-13,14-dihydroretinol + A = all-trans-retinol + AH2
- retinol binding protein (retinol)
Catalysed by MOCOS, RETSAT, RBP1, RBP2cytosolOne of 2 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- L-Alanine:glyoxylate aminotransferase
- Glycodeoxycholate amidohydrolase
Catalysed by MOCOS, AGXT, AGXT2mitochondrial matrix, cytosolOne of 2 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (physeteric acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 8 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- Fatty Acid Beta Oxidation (C12:1->C10:1), Mitochondrial
Catalysed by MOCOS, ACADM, ECHS1, ACAA2 and 1 moremitochondrial matrix
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- L-Alanine:glyoxylate aminotransferase
- tetradecanoyl-CoA + glycine = N-tetradecanoylglycine + CoA + H(+)
Catalysed by MOCOS, AGXT, AGXT2, GLYATL2mitochondrial matrix
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- transport of alanine and glutamine (cytosol to extracellular)
- an acyl-CoA + L-glutamine = an N(2)-acyl-L-glutamine + CoA + H(+)
Catalysed by MOCOS, SLC3A2, SLC7A5, SLC7A10 and 2 moreextracellular space, cytosol
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (7-palmitoleic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 8 routes
- Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O
- amino-acid N-acetyltransferase (N-acetyl-L-alanine)
- long-chain-fatty-acid-CoA ligase (tricosanoic acid)
Catalysed by MOCOS, SLC27A2, ACSL4, ACSL3 and 5 moremitochondrial matrix, cytosolOne of 4 routes