CHEBI:15380

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. Production of 3-Hydroxyoctadecenoylcarnitinec

Catalysed by ALAS1, CPNE7, CPT1A, CPT1C and 1 moremitochondrial matrix, cytosol

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. long-chain-fatty-acid-CoA ligase ((13Z)-eicosenoic acid)

Catalysed by ALAS1, CPNE7, SLC27A2, ACSL4 and 6 moremitochondrial matrix, cytosolOne of 5 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. Carnitine Dimethyl Nonanoyl Transferase, Revsible, Peroxisomal

Catalysed by ALAS1, CPNE7, CRAT, CROTmitochondrial matrix, peroxisomeOne of 3 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. Fatty Acid Beta Oxidation (C16Dc->C14Dc), Peroxisomal

Catalysed by ALAS1, CPNE7, ACAA1, HSD17B4 and 2 moremitochondrial matrix, peroxisome

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. Production of Hexadecanedioylcarnitine

Catalysed by ALAS1, CPNE7, CPT1A, CPT1C and 1 moremitochondrial matrix, cytosolOne of 2 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. fatty-acid-CoA ligase

Catalysed by ALAS1, CPNE7, SLC27A2mitochondrial matrix, cytosolOne of 2 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. medium-chain acyl-CoA ligase (undecylic acid)

Catalysed by ALAS1, CPNE7, ACSM4, ACSM1 and 4 moremitochondrial matrix, cytosolOne of 3 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. long-chain-fatty-acid-CoA ligase (physeteric acid)

Catalysed by ALAS1, CPNE7, SLC27A2, ACSL4 and 6 moremitochondrial matrix, cytosolOne of 8 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. Fatty Acid Beta Oxidation (C12:1->C10:1), Mitochondrial

Catalysed by ALAS1, CPNE7, ACADM, ECHS1 and 2 moremitochondrial matrix

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. acetyl-CoA C-acyltransferase (3-oxo-4(R),8-dimethyl-nonanoyl-CoA)

Catalysed by ALAS1, CPNE7, HADHA, ACAA2 and 1 moremitochondrial matrix

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. long-chain-fatty-acid-CoA ligase (7-palmitoleic acid)

Catalysed by ALAS1, CPNE7, SLC27A2, ACSL4 and 6 moremitochondrial matrix, cytosolOne of 8 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. long-chain-fatty-acid-CoA ligase (tricosanoic acid)

Catalysed by ALAS1, CPNE7, SLC27A2, ACSL4 and 6 moremitochondrial matrix, cytosolOne of 4 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. glycine N-acyltransferase (N-arachidonoylglycine)
3. N(omega)-methyl-L-arginine + glyoxylate = 5-(3-methylguanidino)-2-oxopentanoate + glycine

Catalysed by ALAS1, CPNE7, GLYAT, GLYATL2 and 2 moremitochondrial matrixOne of 2 routes

1. 5-aminolevulinate synthase (2-amino-3-oxoadipate)
2. N-acetylglutamate synthase (N-acetyl-L-cysteine)
3. Mo-molybdopterin + L-cysteine + AH2 = thio-Mo-molybdopterin + L-alanine + A + H2O