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Proteins/UNIPROT:Q00973
Involved in the biosynthesis of gangliosides GM2, GD2, GT2 and GA2 from GM3, GD3, GT3 and GA3, respectively..
Function from UniProtKB (Q00973), read 2026-09-23. CC BY 4.0.
Curated compounds routed: 0
2 rows
79 statements
79 statements · 7 reference databases · Subject: B4GALNT1 · Sources: Bgee, Hetionet, Human Protein Atlas, Human-GEM, Reactome, Rhea, WikiPathways
18 reactions
a beta-D-Gal-(1->4)-beta-D-Glc-(1<->1)-Cer(d18:1(4E))+MAM03110ca ganglioside GA2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92cytosol
Human-GEM MAR00815CC BY 4.0Reference data
a ganglioside GM3 (d18:1(4E))+MAM03110ca ganglioside GM2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
5 names
Resolves to: B4GALNT1
Human-GEM MAR00827CC BY 4.0Reference data
a ganglioside GD3 (d18:1(4E))+MAM03110ca ganglioside GD2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92cytosol
Human-GEM MAR00842CC BY 4.0Reference data
a ganglioside GT3 (d18:1(4E))+MAM03110cMAM02032c+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92cytosol
Human-GEM MAR00856CC BY 4.0Reference data
MAM03110g+MAM03586ga ganglioside GA2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92Golgi apparatus
Human-GEM MAR01351CC BY 4.0Reference data
a beta-D-Gal-(1->4)-beta-D-Glc-(1<->1)-Cer(d18:1(4E))+MAM03110ga ganglioside GA2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92Golgi apparatus
Human-GEM MAR08165CC BY 4.0Reference data
a ganglioside GM3 (d18:1(4E))+MAM03110ga ganglioside GM2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92Golgi apparatus
Human-GEM MAR08190CC BY 4.0Reference data
a ganglioside GD3 (d18:1(4E))+MAM03110ga ganglioside GD2 (d18:1(4E))+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92Golgi apparatus
Human-GEM MAR08191CC BY 4.0Reference data
a ganglioside GT3 (d18:1(4E))+MAM03110gMAM02032g+proton+UDP
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminableEC 2.4.1.92Golgi apparatus
Human-GEM MAR08192CC BY 4.0Reference data
a ganglioside GM3 (d18:1(4E))+UDP-N-acetyl-alpha-D-galactosaminea ganglioside GM2 (d18:1(4E))+UDP+hydron
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminable
Rhea RHEA:12588CC BY 4.0Reference data
a ganglioside GD3 (d18:1(4E))+UDP-N-acetyl-alpha-D-galactosaminea ganglioside GD2 (d18:1(4E))+UDP+hydron
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminable
Rhea RHEA:41816CC BY 4.0Reference data
a ganglioside GM3+UDP-N-acetyl-alpha-D-galactosaminea ganglioside GM2+UDP+hydron
Catalysed by B4GALNT1
Reaction pageLeft to rightBalance undeterminable
Rhea RHEA:43268CC BY 4.0Reference data