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Proteins/UNIPROT:Q9UBR1
Catalyzes a late step in pyrimidine degradation. Converts N-carbamoyl-beta-alanine (3-ureidopropanoate) into beta-alanine, ammonia and carbon dioxide. Likewise, converts N-carbamoyl-beta-aminoisobutyrate (3-ureidoisobutyrate) into beta-aminoisobutyrate, ammonia and carbon dioxide (Probable)..
Function from UniProtKB (Q9UBR1), read 2026-09-23. CC BY 4.0.
Curated compounds routed: 0
1 row
17 statements
17 statements · 7 reference databases · Subject: UPB1 · Sources: Bgee, Hetionet, Human Protein Atlas, Human-GEM, Reactome, Rhea, WikiPathways
4 reactions
N-carbamoyl-beta-alanine+proton+waterbeta-alanine+carbon dioxide+ammonium
Catalysed by UPB1
Reaction pageLeft to rightBalancedEC 3.5.1.6cytosol
Human-GEM MAR04347CC BY 4.0Reference data
3-(carbamoylamino)-2-methylpropanoate+proton+watercarbon dioxide+(R)-3-aminoisobutyric acid
4 names
Resolves to: UPB1
Catalysed by UPB1
Reaction pageLeft to rightBalancedEC 3.5.1.6cytosol
Human-GEM MAR04819CC BY 4.0Reference data
3-(carbamoylamino)propanoate+water+2hydronbeta-alanine+ammonium+carbon dioxide
Catalysed by UPB1
Reaction pageLeft to rightBalanced
Rhea RHEA:11184CC BY 4.0Reference data
3-(carbamoylamino)-2-methylpropanoate+water+2hydron(R)-3-amino-2-methylpropanoate+ammonium+carbon dioxide
Catalysed by UPB1
Reaction pageLeft to rightBalanced
Rhea RHEA:37339CC BY 4.0Reference data