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Proteins/UNIPROT:O75936
Catalyzes the formation of L-carnitine from gamma-butyrobetaine..
Function from UniProtKB (O75936), read 2026-09-23. CC BY 4.0.
Curated compounds routed: 0
9 statements
9 statements · 5 reference databases · Subject: BBOX1 · Sources: Hetionet, Human-GEM, Reactome, Rhea, UniProt
2 reactions
2-oxoglutarate(2-)+4-(trimethylamino)butanoate+dioxygencarbon dioxide+(S)-carnitine+succinate(2-)
Catalysed by BBOX1
Reaction pageLeft to rightBalancedEC 1.14.11.1cytosol
Human-GEM MAR06982CC BY 4.0Reference data
4-(trimethylamino)butanoate+2-oxoglutarate(2-)+dioxygenCHEBI:17126+succinate(2-)
5 names
Resolves to: BBOX1
Catalysed by BBOX1
Reaction pageDirection not assertedBalanced
Rhea RHEA:24028CC BY 4.0Reference data