paraganglioma
Findings
No curated finding names paraganglioma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A benign or malignant neoplasm arising from paraganglia located along the sympathetic or parasympathetic nerves. Infrequently, it may arise outside the usual distribution of the sympathetic and parasympathetic paraganglia. Tumors arising from the adrenal gland medulla are called pheochromocytomas. Morphologically, paragangliomas usually display a nesting (Zellballen) growth pattern. There are no reliable morphologic criteria to distinguish between benign and malignant paragangliomas. The only definitive indicator of malignancy is the presence of regional or distant metastases.
Definition from the Mondo Disease Ontology (MONDO:0000448), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
- Narrower terms (12)
- head and neck paraganglioma
- non-secreting paraganglioma
- parasympathetic paraganglioma
- pheochromocytoma/paraganglioma syndrome 1
- pheochromocytoma/paraganglioma syndrome 2
- pheochromocytoma/paraganglioma syndrome 3
- pheochromocytoma/paraganglioma syndrome 4
- pheochromocytoma/paraganglioma syndrome 5
- pheochromocytoma/paraganglioma syndrome 6
- pheochromocytoma/paraganglioma syndrome 7
- sporadic pheochromocytoma/secreting paraganglioma
- sympathetic paraganglioma
Other names
13 names
Resolves to: paraganglioma
- Also called
- neoplasm of paraganglionneoplasm of the paraganglionparagangliomasparaganglion neoplasmparaganglion tumorparaganglion tumourParaganglionic neoplasmParaganglionic tumorParaganglionic tumourtumor of paragangliontumor of the paragangliontumour of paragangliontumour of the paraganglion