interstitial lung disease
Findings
No curated finding names interstitial lung disease yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A diverse group of lung diseases that affect the lung parenchyma. They are characterized by an initial inflammation of pulmonary alveoli that extends to the interstitium and beyond leading to diffuse pulmonary fibrosis. Interstitial lung diseases are classified by their etiology (known or unknown causes), and radiological-pathological features.
Definition from the Mondo Disease Ontology (MONDO:0015925), read 2026-09-29. CC BY 4.0.
Genes
3 genes
Germline variants in the gene encoding each protein, as classified by GenCC submitters, each in their own words. Limited, disputed and refuted submissions are listed too.
Where it sits
- A kind of
- Narrower terms (14)
- bronchiolitis obliterans syndrome
- bronchiolocentric pattern of interstitial pneumonia
- drug or radiation exposure-related interstitial lung disease
- hypersensitivity pneumonitis
- idiopathic pulmonary fibrosis
- inherited interstitial lung disease
- interstitial lung disease specific to adulthood
- interstitial lung disease specific to childhood
- isolated pulmonary capillaritis
- pneumoconiosis
- pulmonary fibrosis
- pulmonary fibrosis-hepatic hyperplasia-bone marrow hypoplasia syndrome
- radiation pneumonitis
- secondary pulmonary hemosiderosis
Other names
1 name
Resolves to: interstitial lung disease
- Also called
- ILD