Stevens-Johnson syndrome
MONDO:0018229Mondo
Findings
No curated finding names Stevens-Johnson syndrome yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Stevens-Johnson syndrome is a limited form of toxic epidermal necrolysis characterized by destruction and detachment of the skin epithelium and mucous membranes involving less than 10% of the body surface area.
Definition from the Mondo Disease Ontology (MONDO:0018229), read 2026-09-29. CC BY 4.0.
Features
39 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Abnormal blistering of the skinHPOHP:0008066
- Very frequent (80% to 99% of cases)
- AcantholysisHPOHP:0100792
- Very frequent (80% to 99% of cases)
- DiarrheaHPOHP:0002014
- Very frequent (80% to 99% of cases)
- ErythemaHPOHP:0010783
- Very frequent (80% to 99% of cases)
- FatigueHPOHP:0012378
- Very frequent (80% to 99% of cases)
- FeverHPOHP:0001945
- Very frequent (80% to 99% of cases)
- MaculeHPOHP:0012733
- Very frequent (80% to 99% of cases)
- Nausea and vomitingHPOHP:0002017
- Very frequent (80% to 99% of cases)
- Weight lossHPOHP:0001824
- Very frequent (80% to 99% of cases)
- Abnormality of neutrophilsHPOHP:0001874
- Frequent (30% to 79% of cases)
- DysphagiaHPOHP:0002015
- Frequent (30% to 79% of cases)
- Excessive salivationHPOHP:0003781
- Frequent (30% to 79% of cases)
Show the remaining 27
- Abdominal painHPOHP:0002027
- Occasional (5% to 29% of cases)
- Abnormal myocardium morphologyHPOHP:0001637
- Occasional (5% to 29% of cases)
- Abnormal pleura morphologyHPOHP:0002103
- Occasional (5% to 29% of cases)
- Abnormality of the urethraHPOHP:0000795
- Occasional (5% to 29% of cases)
- Acute hepatic failureHPOHP:0006554
- Occasional (5% to 29% of cases)
- AnemiaHPOHP:0001903
- Occasional (5% to 29% of cases)
Where it sits
Other names
2 names
Resolves to: Stevens-Johnson syndrome
- Also called
- Dermatostomatitis, Stevens Johnson typeStevens Johnson syndrome