neoplasm with perivascular epithelioid cell differentiation
MONDO:0006359Mondo
Findings
No curated finding names neoplasm with perivascular epithelioid cell differentiation yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A soft tissue neoplasm composed of perivascular epithelioid cells. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis.
Definition from the Mondo Disease Ontology (MONDO:0006359), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
5 names
Resolves to: neoplasm with perivascular epithelioid cell differentiation
- Also called
- PEComaperivascular epithelioid cell neoplasmperivascular epithelioid cell tumourtumor with perivascular epithelioid cell differentiationtumour with perivascular epithelioid cell differentiation