lymphangiomyoma
MONDO:0006842Mondo
Findings
No curated finding names lymphangiomyoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A neoplasm with perivascular epithelioid cell differentiation, often associated with tuberous sclerosis. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lymph nodes, lung, mediastinum, and retroperitoneum.
Definition from the Mondo Disease Ontology (MONDO:0006842), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
1 name
Resolves to: lymphangiomyoma
- Also called
- lymphangioleiomyoma