idiopathic interstitial pneumonia
MONDO:0002429Mondo
Findings
No curated finding names idiopathic interstitial pneumonia yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A class of diffuse lung diseases that typically affect the pulmonary interstitium, although some also have a component affecting the airways (for instance, Cryptogenic organizing pneumonitis).
Definition from the Mondo Disease Ontology (MONDO:0002429), read 2026-09-29. CC BY 4.0.
Features
1 feature
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, hp/releases/2026-09-01.
- PneumoniaMondoHP:0002090
Where it sits
- A kind of
- Narrower terms (10)
- acute interstitial pneumonia
- combined pulmonary fibrosis-emphysema syndrome
- cryptogenic organizing pneumonia
- desquamative interstitial pneumonia
- follicular bronchiolits
- idiopathic pleuroparenchymal fibroelastosis
- idiopathic pulmonary fibrosis
- lymphoid interstitial pneumonia
- non-specific interstitial pneumonia
- respiratory bronchiolitis-interstitial lung disease syndrome
Other names
4 names
Resolves to: idiopathic interstitial pneumonia
- Also called
- idiopathic fibrosing alveolitisidiopathic interstitial pneumonitisIIPnoninfectious pneumonia