desquamative interstitial pneumonia
MONDO:0009887Mondo
Findings
No curated finding names desquamative interstitial pneumonia yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.
Definition from the Mondo Disease Ontology (MONDO:0009887), read 2026-09-29. CC BY 4.0.
- Inheritance
- Autosomal recessive inheritance
HPO, annotations 2026-09-02
Features
2 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Desquamative interstitial pneumonitisHPOHP:0005942
- Type II pneumocyte hypertrophyHPOHP:0033246
Where it sits
- A kind of
Other names
2 names
Resolves to: desquamative interstitial pneumonia
- Also called
- RBILDrespiratory bronchiolitis interstitial lung disease