dermatitis herpetiformis, familial
Findings
No curated finding names dermatitis herpetiformis, familial yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Dermatitis herpetiformis is a rare, chronic, skin disorder characterized by groups of severely itchy blisters and raised skin lesions. These are more common on the knees, elbows, buttocks and shoulder blades. The slow onset of symptoms usually begins during adulthood, but children can also be affected. Other symptoms mayinclude fluid-filled sores; red lesions that resemble hives; and itchiness, rednessand burning. The exact cause of this disease is not known,but it is frequently associated with the inability to digest gluten. People with this disease are typically treated with the drug dapsone.
Definition from the Mondo Disease Ontology (MONDO:0011024), read 2026-09-29. CC BY 4.0.
Features
1 feature
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- PruritusHPOHP:0000989
Where it sits
Other names
1 name
Resolves to: dermatitis herpetiformis, familial
- Also called
- hereditary dermatitis herpetiformis