dermatitis herpetiformis
Findings
No curated finding names dermatitis herpetiformis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Dermatitis herpetiformis (DH) is a chronic autoimmune subepidermal bullous disease characterized by grouped pruritic lesions such as papules, urticarial plaques, erythema, and herpetiform vesiculae, with a predominantly symmetrical distribution on extensor surfaces of the elbows (90%), knees (30%), shoulders, buttocks, sacral region, and face of children and adults. Erosions, excoriations and hyperpigmentation usually follow. DH may also appear as a consequence of gluten intolerance.
Definition from the Mondo Disease Ontology (MONDO:0015614), read 2026-09-29. CC BY 4.0.
Features
26 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Abnormal blistering of the skinHPOHP:0008066
- Very frequent (80% to 99% of cases)
- AutoimmunityHPOHP:0002960
- Very frequent (80% to 99% of cases)
- ErythemaHPOHP:0010783
- Very frequent (80% to 99% of cases)
- Gluten intoleranceHPOHP:0012538
- Very frequent (80% to 99% of cases)
- MaculeHPOHP:0012733
- Very frequent (80% to 99% of cases)
- MalabsorptionHPOHP:0002024
- Very frequent (80% to 99% of cases)
- Microcytic anemia
Show the remaining 14
- Anti-epidermal transglutaminase antibody positivityHPOHP:0033565
- Frequent (30% to 79% of cases)
- Anti-reticulin antibody positivityHPOHP:4000030
- Frequent (30% to 79% of cases)
- Anti-transglutaminase 6 antibodyHPOHP:4000026
- Frequent (30% to 79% of cases)
- Anti-type VII collagen antibodyHPOHP:4000031
- Frequent (30% to 79% of cases)
- Antigliadin antibody positivityHPOHP:4000029
- Frequent (30% to 79% of cases)
- Eczematoid dermatitisHPOHP:0000964
Where it sits
- A kind of
- Narrower terms (2)
Other names
2 names
Resolves to: dermatitis herpetiformis
- Also called
- Duhring's diseaseDurhing-Brocq disease