arrhythmogenic right ventricular dysplasia 11

Findings

No curated finding names arrhythmogenic right ventricular dysplasia 11 yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.

Definition

Inheritance

Autosomal dominant inheritance

Onset and course

Late onset · Middle age onset · Juvenile onset · Young adult onset

HPO, annotations 2026-09-02

What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.

Germline variants in the gene encoding each protein, as classified by GenCC submitters, each in their own words. Limited, disputed and refuted submissions are listed too.

Where it sits

A kind of

• familial isolated arrhythmogenic right ventricular dysplasia

Resolves to: arrhythmogenic right ventricular dysplasia 11

Also called

arrhythmogenic right ventricular cardiomyopathy 11arrhythmogenic right ventricular dysplasia 11 with mild palmoplantar keratoderma and woolly hairarrhythmogenic right ventricular dysplasia 11 with mild palmoplantar keratoderma and wooly hairarrhythmogenic right ventricular dysplasia type 11arrhythmogenic right ventricular dysplasia, familial, type 11ARVC11ARVD11DSC2 familial isolated arrhythmogenic right ventricular dysplasiafamilial isolated arrhythmogenic right ventricular dysplasia caused by mutation in DSC2