MIMS2

Mitochondrial inner membrane adapter protein essential for terminal erythroid differentiation and heme biosynthesis. Facilitates formation of an oligomeric mitochondrial iron transport complex required for iron acquisition during heme synthesis, although it does not function as a direct iron transporter (By similarity). Directly interacts with terminal heme synthesis enzymes PPOX and FECH to enhance ferrochelatase activity and couple iron import with heme synthesis (By similarity). Regulates mitochondrial energy metabolism through interaction with ATP synthase subunits..

Function from UniProtKB (Q96KR6), read 2026-09-23. CC BY 4.0.