Proteins/UNIPROT:Q9BXV9

GON7

ProteinUNIPROT:Q9BXV9

Component of the EKC/KEOPS complex that is required for the formation of a threonylcarbamoyl group on adenosine at position 37 (t(6)A37) in tRNAs that read codons beginning with adenine. The complex is probably involved in the transfer of the threonylcarbamoyl moiety of threonylcarbamoyl-AMP (TC-AMP) to the N6 group of A37. GON7 plays a supporting role to the catalytic subunit OSGEP in the complex..

Function from UniProtKB (Q9BXV9), read 2026-09-23. CC BY 4.0.

Curated compounds routed: 0

What the reference databases state

GenCC submitters' classifications

1 row

Galloway-Mowat syndrome 9 has a germline basis in GON7DiseaseGenCC HGNC:20356|MONDO:0030471Inferred only

Statements

6 statements

6 statements · 2 reference databases · Subject: GON7 · Sources: Hetionet, Reactome

Order

GON7 covaries with YIF1AProteinHetionet hetionet:covaries:10897-84520Inferred only
ZNF514 covaries with GON7ProteinHetionet hetionet:covaries:84520-84874Inferred only
ZNF555 covaries with GON7ProteinHetionet hetionet:covaries:148254-84520Inferred only
GON7 participates in Metabolism of RNAPathwayReactome R-HSA-8953854Inferred only
GON7 participates in tRNA modification in the nucleus and cytosolPathwayReactome R-HSA-6782315Inferred only
GON7 participates in tRNA processingPathwayReactome R-HSA-72306Inferred only

Other names

1 name

Resolves to: GON7

Also called: EKC/KEOPS complex subunit GON7

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