wooly hair nevus
Findings
No curated finding names wooly hair nevus yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Woolly hair nevus (WHN) is a rare non-familial hair anomaly characterized by kinky, tightly coiled, and hypopigmented fine hair with an average diameter of 0.5 cm, noted, since birth or during the first two years of life, in a localized circumscribed distribution on the scalp. Occasionally, WHN grows in areas observed to be alopecic in the neonatal period. WHN can be associated with features like ocular defects (persistent pupillary membrane, retinal defects), precocious puberty, and epidermal nevi.
Definition from the Mondo Disease Ontology (MONDO:0019311), read 2026-09-29. CC BY 4.0.
Features
12 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Curly hairHPOHP:0002212
- Very frequent (80% to 99% of cases)
- Fine hairHPOHP:0002213
- Very frequent (80% to 99% of cases)
- Patchy hypopigmentation of hairHPOHP:0011365
- Very frequent (80% to 99% of cases)
- Woolly scalp hairHPOHP:0040149
- Very frequent (80% to 99% of cases)
- Congenital posterior occipital alopeciaHPOHP:0007534
- Frequent (30% to 79% of cases)
- Verrucous epidermal nevusHPOHP:0034275
- Frequent (30% to 79% of cases)
Where it sits
- A kind of