vulval Paget disease
Findings
No curated finding names vulval Paget disease yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
An uncommon intraepithelial malignant neoplasm of eccrine or apocrine origin, arising from the vulva. It usually affects post-menopausal women. In approximately 10-20% of the cases there is an associated anorectal, or urothelial carcinoma or a skin appendage adenocarcinoma identified. It presents as a red, eczematous lesion. Microscopically, it is characterized by the presence of the typical Paget cells which are large, round cells with abundant cytoplasm and prominent nuclei.
Definition from the Mondo Disease Ontology (MONDO:0002207), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
7 names
Resolves to: vulval Paget disease
- Also called
- mammalian vulva Paget diseasePaget disease of the vulvaPaget's disease of the vulvaPaget's disease of vulvavulva Paget's diseasevulval Paget's diseasevulvar Paget's disease