torsade-de-pointes syndrome with short coupling interval
MONDO:0013317Mondo
Findings
No curated finding names torsade-de-pointes syndrome with short coupling interval yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Torsade-de-pointes (TdP) syndrome with short coupling interval is a very rare variant of Torsade de pointes, a polymorphic ventricular tachycardia, which is characterized by a short coupling interval of the first TdP beat on electrocardiogram in the absence of any structural heart disease. It manifests in early adulthood with syncope, often results in ventricular fibrillation and shows a high risk of sudden cardiac death.
Definition from the Mondo Disease Ontology (MONDO:0013317), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of