small intestinal enteropathy-associated T-cell lymphoma
Findings
No curated finding names small intestinal enteropathy-associated T-cell lymphoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
An enteropathy-associated T-cell lymphoma arising from the small intestine, most commonly the jejunum or ileum. Patients usually present with abdominal pain, often associated with intestinal perforation. There is often a history of celiac disease. The lymphoma cells are usually medium-sized to large and form an ulcerating mucosal lesion with invasion of the small intestinal wall. Villous atrophy is present in the adjacent small intestinal mucosa. In a minority of cases the lymphoma cells are medium-sized and form a monomorphic infiltrate.
Definition from the Mondo Disease Ontology (MONDO:0006418), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
4 names
Resolves to: small intestinal enteropathy-associated T-cell lymphoma
- Also called
- enteropathy-associated T-cell lymphoma of small intestinesmall intestinal EATLsmall intestinal enteropathy-type T-cell lymphomasmall intestine enteropathy-associated T-cell lymphoma