secondary intestinal lymphangiectasia
Findings
No curated finding names secondary intestinal lymphangiectasia yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Secondary intestinal lymphangiectasia is an acquired from of intestinal lymphangiectasia manifesting as a protein-losing enteropathy due to another disorder such as CrohnBs disease, congestive heart failure, sarcoidosis, Turner syndrome and often in patients who have undergone a Fontan operation. It is characterized by malabsorption, diarrhea, edema due hypoproteinemia, steatorrhea and serosal effusions.
Definition from the Mondo Disease Ontology (MONDO:0019574), read 2026-09-29. CC BY 4.0.
Features
40 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Increased stool alpha1-antitrypsin concentrationHPOHP:0031686
- Very frequent (80% to 99% of cases)
- LymphedemaHPOHP:0001004
- Very frequent (80% to 99% of cases)
- Chronic diarrheaHPOHP:0002028
- Frequent (30% to 79% of cases)
- Decreased total lymphocyte countHPOHP:0001888
- Frequent (30% to 79% of cases)
- EdemaHPOHP:0000969
- Frequent (30% to 79% of cases)
- FatigueHPOHP:0012378
- Frequent (30% to 79% of cases)
- Hypocholesterolemia
Show the remaining 28
- AutoimmunityHPOHP:0002960
- Occasional (5% to 29% of cases)
- Celiac diseaseHPOHP:0002608
- Occasional (5% to 29% of cases)
- Chylous ascitesHPOHP:0012281
- Occasional (5% to 29% of cases)
- CirrhosisHPOHP:0001394
- Occasional (5% to 29% of cases)
- Constrictive pericarditisHPOHP:0002563
- Occasional (5% to 29% of cases)
- Decreased circulating IgA concentrationHPOHP:0002720
- Occasional (5% to 29% of cases)
Where it sits
- A kind of