right superior vena cava connecting to left-sided atrium
Findings
No curated finding names right superior vena cava connecting to left-sided atrium yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Right superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by the right SVC passing medially and dorsally to the aortic root and draining into the left atrium. Patients usually present a right-to-left systemic venous blood shunt which may manifest with arterial hypoxemia, cyanosis, exercise dyspnea, clubbing of the fingers, palpitations, murmurs and/or potentially fatal brain abscess. Association with other cardiac anomalies has been reported.
Definition from the Mondo Disease Ontology (MONDO:0020441), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
2 names
Resolves to: right superior vena cava connecting to left-sided atrium
- Also called
- right superior caval vein connecting to left-sided atriumright SVC connecting to left-sided atrium