Rasmussen subacute encephalitis
MONDO:0016019Mondo
Findings
No curated finding names Rasmussen subacute encephalitis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare, progressive chronic inflammation of a single cerebral hemisphere that usually affects children. It is characterized by severe seizures, loss of motor skills and speech, hemiparesis, and dementia.
Definition from the Mondo Disease Ontology (MONDO:0016019), read 2026-09-29. CC BY 4.0.
Features
48 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Focal-onset seizureHPOHP:0007359
- Very frequent (80% to 99% of cases)
- Functional motor deficitHPOHP:0004302
- Very frequent (80% to 99% of cases)
- AutoimmunityHPOHP:0002960
- Frequent (30% to 79% of cases)
- Cerebral cortical hemiatrophyHPOHP:0100308
- Frequent (30% to 79% of cases)
- Cognitive impairmentHPOHP:0100543
- Frequent (30% to 79% of cases)
- EEG with focal sharp slow wavesHPOHP:0011195
- Frequent (30% to 79% of cases)
- EEG with focal spikesHPOHP:0011193
- Frequent (30% to 79% of cases)
- Epilepsia partialis continuaHPOHP:0012847
- Frequent (30% to 79% of cases)
- Focal aware seizureHPOHP:0002349
- Frequent (30% to 79% of cases)
- Focal impaired awareness seizureHPOHP:0002384
- Frequent (30% to 79% of cases)
- Focal motor seizureHPOHP:0011153
- Frequent (30% to 79% of cases)
- HemiparesisHPOHP:0001269
- Frequent (30% to 79% of cases)
Show the remaining 36
- Involuntary movementsHPOHP:0004305
- Frequent (30% to 79% of cases)
- Repeated focal motor seizuresHPOHP:0032665
- Frequent (30% to 79% of cases)
- Subcortical cerebral atrophyHPOHP:0012157
- Frequent (30% to 79% of cases)
- VentriculomegalyHPOHP:0002119
- Frequent (30% to 79% of cases)
- Abnormal basal ganglia morphologyHPOHP:0002134
- Occasional (5% to 29% of cases)
- Abnormal cerebrospinal fluid morphologyHPOHP:0002921
- Occasional (5% to 29% of cases)
Where it sits
Other names
6 names
Resolves to: Rasmussen subacute encephalitis
- Also called
- CFEchronic focal encephalitisRasmussen EncephalitisRasmussen syndromeRasmussen’s encephalitisRasmussen’s syndrome