punctate palmoplantar keratoderma type III
MONDO:0007047Mondo
Findings
No curated finding names punctate palmoplantar keratoderma type III yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Acrokeratoelastoidosis of Costa is a rare dermatosis characterized by small, firm papules or plaques (resembling warts) on the sides of the hands and feet. These stationary and asymptomatic lesions appear generally at puberty, or sometimes later
Definition from the Mondo Disease Ontology (MONDO:0007047), read 2026-09-29. CC BY 4.0.
Features
12 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Epidermal acanthosisHPOHP:0025092
- Very frequent (80% to 99% of cases)
- Fragmented elastic fibers in the dermisHPOHP:0025167
- Very frequent (80% to 99% of cases)
- Hyperkeratotic papuleHPOHP:0045059
- Very frequent (80% to 99% of cases)
- Palmoplantar hyperkeratosisHPOHP:0000972
- Very frequent (80% to 99% of cases)
- GranulomatosisHPOHP:0002955
- Frequent (30% to 79% of cases)
- HypergranulosisHPOHP:0025114
- Frequent (30% to 79% of cases)
- OrthokeratosisHPOHP:0040162
- Frequent (30% to 79% of cases)
- Yellow papuleHPOHP:0025507
- Frequent (30% to 79% of cases)
- Palmar hyperhidrosisHPOHP:0006089
- Occasional (5% to 29% of cases)
- Piezogenic pedal papulesHPOHP:0025509
- Occasional (5% to 29% of cases)
- Skin plaqueHPOHP:0200035
- Occasional (5% to 29% of cases)
- Abnormality of the lower limbHPOHP:0002814
- Very rare (1% to 4% of cases)
Where it sits
- A kind of
Other names
6 names
Resolves to: punctate palmoplantar keratoderma type III
- Also called
- acrokeratoelastoidosis of CostaAKEkeratoderma, palmoplantar, punctate type 3PPKP3punctate palmoplantar hyperkeratosis type 3punctate palmoplantar keratoderma type 3