pulmonary interstitial glycogenosis
MONDO:0016321Mondo
Findings
No curated finding names pulmonary interstitial glycogenosis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Pulmonary interstitial glycogenosis (PIG) is a rare non-lethal pediatric form of interstitial lung disease (ILD).
Definition from the Mondo Disease Ontology (MONDO:0016321), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
2 names
Resolves to: pulmonary interstitial glycogenosis
- Also called
- infantile cellular interstitial pneumonitisPIG