pulmonary artery coming from the aorta
Findings
No curated finding names pulmonary artery coming from the aorta yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Pulmonary artery coming from the aorta (PACA) is a cardiac malformation characterized by anomalous origin of one branch of the pulmonary arteries from the ascending aorta and a normal origin of the other pulmonary artery from the right ventricular outflow tract, and presenting with respiratory distress, congestive heart failure and failure to thrive within the first days/months of life.
Definition from the Mondo Disease Ontology (MONDO:0020391), read 2026-09-29. CC BY 4.0.
Features
26 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Abnormal cardiovascular system morphologyHPOHP:0030680
- Very frequent (80% to 99% of cases)
- Anomalous origin of right pulmonary artery from ascending aortaHPOHP:0005143
- Very frequent (80% to 99% of cases)
- Atrial septal defectHPOHP:0001631
- Frequent (30% to 79% of cases)
- Congestive heart failureHPOHP:0001635
- Frequent (30% to 79% of cases)
- CyanosisHPOHP:0000961
- Frequent (30% to 79% of cases)
- Exertional dyspneaHPOHP:0002875
- Frequent (30% to 79% of cases)
Show the remaining 14
- Abnormal aortic arch morphologyHPOHP:0012303
- Occasional (5% to 29% of cases)
- Anomalous origin of left pulmonary artery from ascending aortaHPOHP:0011661
- Occasional (5% to 29% of cases)
- Aortopulmonary windowHPOHP:0011604
- Occasional (5% to 29% of cases)
- Heart murmurHPOHP:0030148
- Occasional (5% to 29% of cases)
- Pulmonary arterial hypertensionHPOHP:0002092
- Occasional (5% to 29% of cases)
- Tetralogy of FallotHPOHP:0001636
Where it sits
Other names
2 names
Resolves to: pulmonary artery coming from the aorta
- Also called
- abnormal origin of right or left pulmonary artery from the aortahemitruncus arteriosus