pulmonary alveolar proteinosis
MONDO:0001437Mondo
Findings
No curated finding names pulmonary alveolar proteinosis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare lung disorder characterized by the filling of the pulmonary alveoli with proteinaceous material which stains positive with periodic acid-Schiff stain. It may be idiopathic or secondary due to hematologic malignancies or the inhalation of mineral dusts. Signs and symptoms include dyspnea, cough and low grade fever.
Definition from the Mondo Disease Ontology (MONDO:0001437), read 2026-09-29. CC BY 4.0.
Features
1 feature
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, hp/releases/2026-09-01.
- Intraalveolar phospholipid accumulationMondoHP:0006517
Where it sits
- A kind of