pseudoxanthoma elasticum-like papillary dermal elastolysis
Findings
No curated finding names pseudoxanthoma elasticum-like papillary dermal elastolysis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Pseudoxanthoma elasticum-like papillary dermal elastolysis (PXE-PDE) is a rare, acquired, idiopathic dermal tissue disorder characterized by numerous, asymptomatic, 2-3 mm, yellowish, non-follicular papules that tend to converge into cobblestone-like plaques which are distributed symmetrically over the posterior neck, supraclavicular region, axillae, and sometimes abdomen. Unlike PXE, these skin lesions show select elimination (absence or marked loss) of elastic fibers in the papillary dermis and there is no systemic involvement.
Definition from the Mondo Disease Ontology (MONDO:0016448), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
2 names
Resolves to: pseudoxanthoma elasticum-like papillary dermal elastolysis
- Also called
- PXE-like papillary dermal elastolysisPXE-PDE