progressive deafness with stapes fixation
Findings
No curated finding names progressive deafness with stapes fixation yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Stapes fixation (stapedovestibular ankylosis) is a hearing loss condition that appears as a consequence of annular ligament destruction followed by excessive connective tissue production during the healing process. This condition is mainly observed in otosclerosis, but is also found in chronic otitis media with tympanosclerosis, and other rare bone diseases such as Paget's disease and osteogenesis imperfecta (Lobstein disease).
Definition from the Mondo Disease Ontology (MONDO:0011080), read 2026-09-29. CC BY 4.0.
Features
2 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Bilateral conductive hearing impairmentHPOHP:0008513
- Very frequent (80% to 99% of cases)
- Stapes ankylosisHPOHP:0000381
- Very frequent (80% to 99% of cases)
Where it sits
- A kind of
Other names
2 names
Resolves to: progressive deafness with stapes fixation
- Also called
- Stapedo-vestibular ankylosisThies-Reis syndrome