primary effusion lymphoma
MONDO:0018842Mondo
Findings
No curated finding names primary effusion lymphoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A large B-cell lymphoma located in the body cavities, characterized by pleural, peritoneal, and pericardial fluid lymphomatous effusions and that is always associated with human herpes virus-8 (HHV-8).
Definition from the Mondo Disease Ontology (MONDO:0018842), read 2026-09-29. CC BY 4.0.
Features
8 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Abdominal distentionHPOHP:0003270
- Very frequent (80% to 99% of cases)
- Abdominal painHPOHP:0002027
- Very frequent (80% to 99% of cases)
- Abnormal peritoneum morphologyHPOHP:0002585
- Very frequent (80% to 99% of cases)
- B-cell lymphomaHPOHP:0012191
- Very frequent (80% to 99% of cases)
- DyspneaHPOHP:0002094
- Very frequent (80% to 99% of cases)
- Pericardial effusionHPOHP:0001698
- Very frequent (80% to 99% of cases)
- Pleural effusionHPOHP:0002202
- Very frequent (80% to 99% of cases)
- ImmunodeficiencyHPOHP:0002721
- Frequent (30% to 79% of cases)
Where it sits
Other names
2 names
Resolves to: primary effusion lymphoma
- Also called
- body cavity-based lymphomaPEL