primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma
Findings
No curated finding names primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma is a rare form of primary cutaneous T-cell lymphoma characterized by rapidly progressing, localized or disseminated nodules, tumors or eczematous skin lesions. It has a particularly aggressive clinical course with a high tendency to spread, in advanced stages, to extracutaneous locations (the central nervous system, lung, testes). Lymph nodes are often spared.
Definition from the Mondo Disease Ontology (MONDO:0015811), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
2 names
Resolves to: primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma
- Also called
- Berti lymphomaprimary cutaneous epidermotropic cytotoxic CD8+ T-cell lymphoma