persistent left superior vena cava connecting to the left-sided atrium
Findings
No curated finding names persistent left superior vena cava connecting to the left-sided atrium yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Persistent left superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by a persistent left superior vena cava which drains directly to the left atrium, without passing through the coronary sinus (that may be absent in some cases). Patients are usually asymptomatic and discovered incidentally, however hypoxia, cyanosis, murmurs, palpitations, cardiac structural anomalies (e.g. atrial septal defect, bicuspid aortic valve, cor triatrium) and risk of paradoxical embolization may be associated.
Definition from the Mondo Disease Ontology (MONDO:0020440), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
3 names
Resolves to: persistent left superior vena cava connecting to the left-sided atrium
- Also called
- left superior caval vein persisting to the left-sided atriumpersistent left superior caval vein connecting to the left-sided atriumpersistent left SVC connecting to the left-sided atrium