pemphigus erythematosus
Findings
No curated finding names pemphigus erythematosus yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Pemphigus erythematosus is a rare superficial pemphigus disease characterized clinically by well-demarcated, localized, erythematous, scaly, hyperkeratotic, crusted plaques, with frequent butterfly distribution over the malar area of the face (but also commonly involving trunk and scalp, and less frequently the extremities, with a photoexposed distribution). Histologically, granular deposits along the dermal-epidermal junction, in addition to intercellular deposition in the upper epidermis, are observed.
Definition from the Mondo Disease Ontology (MONDO:0019323), read 2026-09-29. CC BY 4.0.
Features
14 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- AcantholysisHPOHP:0100792
- Very frequent (80% to 99% of cases)
- AutoimmunityHPOHP:0002960
- Very frequent (80% to 99% of cases)
- Erythematous plaqueHPOHP:0025474
- Very frequent (80% to 99% of cases)
- Localized skin lesionHPOHP:0011355
- Very frequent (80% to 99% of cases)
- Malar rashHPOHP:0025300
- Very frequent (80% to 99% of cases)
- Abnormal blistering of the skinHPOHP:0008066
- Frequent (30% to 79% of cases)
- Antinuclear antibody positivity
Show the remaining 2
- Skin erosionHPOHP:0200041
- Occasional (5% to 29% of cases)
- Systemic lupus erythematosusHPOHP:0002725
- Occasional (5% to 29% of cases)
Where it sits
- A kind of
Other names
2 names
Resolves to: pemphigus erythematosus
- Also called
- seborrheic pemphigusSenear-Usher syndrome