nodular cutaneous amyloidosis
Findings
No curated finding names nodular cutaneous amyloidosis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as SjC6grenBs syndrome and CREST syndrome.
Definition from the Mondo Disease Ontology (MONDO:0015302), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
5 names
Resolves to: nodular cutaneous amyloidosis
- Also called
- amyloidosis nodular localised cutaneousamyloidosis nodular localized cutaneousPLCNAprimary localised cutaneous nodular amyloidosisprimary localized cutaneous nodular amyloidosis