marginal zone lymphoma
Findings
No curated finding names marginal zone lymphoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A usually indolent mature B-cell lymphoma, arising from the marginal zone of lymphoid tissues. It is characterized by the presence of small to medium sized atypical lymphocytes. It comprises three entities, according to the anatomic sites involved: extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue, which affects extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal zone B-cell lymphoma, which affects lymph nodes without evidence of extranodal disease; and splenic marginal zone B-cell lymphoma, which affects the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood.
Definition from the Mondo Disease Ontology (MONDO:0017604), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
5 names
Resolves to: marginal zone lymphoma
- Also called
- lymphoma of marginal zone B cellmarginal zone B cell lymphomamarginal zone B-cell lymphomaMZBCLMZL