lymphoplasmacytic inflammatory pseudotumor of the liver
Findings
No curated finding names lymphoplasmacytic inflammatory pseudotumor of the liver yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A subtype of inflammatory pseudotumor of the liver characterized by a benign, well-circumscribed tumor with diffuse lymphoplasmacytic infiltration with histological features of IgG4-related disease (numerous IgG4-positive plasma cells, prominent eosinophils, stromal fibrosis, fibroblastic proliferations and, frequently, obliterative phlebitis), and that is likely located around the hepatic hilum. Most often it is discovered as an incidental finding.
Definition from the Mondo Disease Ontology (MONDO:0035313), read 2026-09-29. CC BY 4.0.
Where it sits
Other names
1 name
Resolves to: lymphoplasmacytic inflammatory pseudotumor of the liver
- Also called
- IgG4-related inflammatory pseudotumor of the liver