lipomatous non-saccular limited dorsal myeloschisis
MONDO:0970960Mondo
Findings
No curated finding names lipomatous non-saccular limited dorsal myeloschisis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare non-saccular limited dorsal myeloschisis histologically characterized by skin tissue with a jagged depression of squamous epithelium continued to subcutaneous mature adipose tissue with loose connective tissue. GFAP-immunopositive glial cells are embedded in the subcutaneous lipoma. The extradural and intradural stalk have cord-like fibrocollagenous tissue containing adipose tissue, peripheral nerve fibers, clusters of melanocytes, and skeletal muscle fibers.
Definition from the Mondo Disease Ontology (MONDO:0970960), read 2026-09-29. CC BY 4.0.