linear atrophoderma of Moulin
Findings
No curated finding names linear atrophoderma of Moulin yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Linear atrophoderma of Moulin (LAM) is characterized by mildly atrophic and hyperpigmented band-like lesions that follow the lines of Blaschko on the trunk or limbs. Since its initial description in 1992, less than 30 cases have been reported in the literature. Onset occurs during childhood or adolescence and the disease is non-progressive. There is no prior inflammation or subsequent scleroderma. The etiology is unknown but as LAM follows the lines of Blaschko it has been suggested that the disease is caused by mosaicism of a predisposing gene.
Definition from the Mondo Disease Ontology (MONDO:0015371), read 2026-09-29. CC BY 4.0.
Features
1 feature
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Linear hyperpigmentationHPOHP:0007546
- Obligate (100% of cases)
Reported absent (4)
- Inflammatory abnormality of the skinHPOHP:0011123
- PruritusHPOHP:0000989
- SclerodermaHPOHP:0100324
- Stiff skinHPOHP:0030053
Where it sits
- A kind of