leiomyosarcoma
MONDO:0005058Mondo
Findings
No curated finding names leiomyosarcoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
An uncommon, aggressive malignant smooth muscle neoplasm, usually occurring in post-menopausal women. It is characterized by a proliferation of neoplastic spindle cells. Morphologic variants include epithelioid, granular cell, inflammatory and myxoid leimyosarcomas.
Definition from the Mondo Disease Ontology (MONDO:0005058), read 2026-09-29. CC BY 4.0.
Genes
2 genes
Germline variants in the gene encoding each protein, as classified by GenCC submitters, each in their own words. Limited, disputed and refuted submissions are listed too.
Where it sits
- Narrower terms (31)
- bone leiomyosarcoma
- breast leiomyosarcoma
- central nervous system leiomyosarcoma
- colon leiomyosarcoma
- conventional leiomyosarcoma
- cutaneous leiomyosarcoma
- epithelioid leiomyosarcoma
- esophagus leiomyosarcoma
- fallopian tube leiomyosarcoma
- gallbladder leiomyosarcoma
- gastric leiomyosarcoma
- heart leiomyosarcoma
- inflammatory leiomyosarcoma
- kidney leiomyosarcoma
- laryngeal leiomyosarcoma
- leiomyosarcoma of the cervix uteri
- leiomyosarcoma of the corpus uteri
- liver leiomyosarcoma
- lung leiomyosarcoma
- mediastinum leiomyosarcoma
Other names
4 names
Resolves to: leiomyosarcoma
- Also called
- leiomyosarcoma - not uterineleiomyosarcoma (excluding uterine leiomyosarcoma)leiomyosarcoma, malignantLeiomyosarcomas