Kawasaki disease
MONDO:0012727Mondo
Findings
No curated finding names Kawasaki disease yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated.
Definition from the Mondo Disease Ontology (MONDO:0012727), read 2026-09-29. CC BY 4.0.
Features
46 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Cervical lymphadenopathyHPOHP:0025289
- Very frequent (80% to 99% of cases)
- CheilitisHPOHP:0100825
- Very frequent (80% to 99% of cases)
- ConjunctivitisHPOHP:0000509
- Very frequent (80% to 99% of cases)
- Palmoplantar erythemaHPOHP:0025493
- Very frequent (80% to 99% of cases)
- ProteinuriaHPOHP:0000093
- Very frequent (80% to 99% of cases)
- Recurrent pharyngitisHPOHP:0100776
- Very frequent (80% to 99% of cases)
- Skin rashHPOHP:0000988
- Very frequent (80% to 99% of cases)
- VasculitisHPOHP:0002633
- Very frequent (80% to 99% of cases)
- Abdominal painHPOHP:0002027
- Frequent (30% to 79% of cases)
- Abnormal heart valve morphologyHPOHP:0001654
- Frequent (30% to 79% of cases)
- Abnormality of nail colorHPOHP:0100643
- Frequent (30% to 79% of cases)
- ArthritisHPOHP:0001369
- Frequent (30% to 79% of cases)
Show the remaining 34
- Conjunctival hyperemiaHPOHP:0030953
- Frequent (30% to 79% of cases)
- DiarrheaHPOHP:0002014
- Frequent (30% to 79% of cases)
- EdemaHPOHP:0000969
- Frequent (30% to 79% of cases)
- Elevated circulating C-reactive protein concentrationHPOHP:0011227
- Frequent (30% to 79% of cases)
- Elevated erythrocyte sedimentation rateHPOHP:0003565
- Frequent (30% to 79% of cases)
- FatigueHPOHP:0012378
- Frequent (30% to 79% of cases)
Where it sits
- A kind of
Other names
5 names
Resolves to: Kawasaki disease
- Also called
- acute febrile mucocutaneous lymph node syndromeacute febrile mucocutaneous lymph node syndrome [MCLS]infantile polyarteritis nodosaKawasaki syndromemucocutaneous lymph node syndrome