kaposiform lymphangiomatosis
MONDO:0018736Mondo
Findings
No curated finding names kaposiform lymphangiomatosis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A generalized lymphatic anomaly characterized by kaposiform spindled lymphatic endothelial cells.
Definition from the Mondo Disease Ontology (MONDO:0018736), read 2026-09-29. CC BY 4.0.
Features
46 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Abnormal lung morphologyHPOHP:0002088
- Very frequent (80% to 99% of cases)
- Abnormal lymphatic vessel morphologyHPOHP:0100766
- Very frequent (80% to 99% of cases)
- Abnormal mediastinum morphologyHPOHP:0045026
- Very frequent (80% to 99% of cases)
- Abnormality of the lymphatic systemHPOHP:0100763
- Very frequent (80% to 99% of cases)
- Pleural effusionHPOHP:0002202
- Very frequent (80% to 99% of cases)
- Abnormal bleedingHPOHP:0001892
- Frequent (30% to 79% of cases)
- Abnormal skeletal morphologyHPOHP:0011842
- Frequent (30% to 79% of cases)
- Abnormal spleen morphologyHPOHP:0025408
- Frequent (30% to 79% of cases)
- Abnormal thorax morphologyHPOHP:0000765
- Frequent (30% to 79% of cases)
- Abnormality of the respiratory systemHPOHP:0002086
- Frequent (30% to 79% of cases)
- CoughHPOHP:0012735
- Frequent (30% to 79% of cases)
- DyspneaHPOHP:0002094
- Frequent (30% to 79% of cases)
Show the remaining 34
- HypofibrinogenemiaHPOHP:0011900
- Frequent (30% to 79% of cases)
- OsteolysisHPOHP:0002797
- Frequent (30% to 79% of cases)
- Pericardial effusionHPOHP:0001698
- Frequent (30% to 79% of cases)
- Abnormal femur morphologyHPOHP:0002823
- Occasional (5% to 29% of cases)
- Abnormal humerus morphologyHPOHP:0031095
- Occasional (5% to 29% of cases)
- Abnormal ischium morphologyHPOHP:0003174
- Occasional (5% to 29% of cases)
Where it sits
- A kind of