kaposiform hemangioendothelioma
MONDO:0016236Mondo
Findings
No curated finding names kaposiform hemangioendothelioma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Kaposiform hemangioendothelioma is a very rare, aggressive, vascular tumor manifesting in the neonatal period or in infancy as cutaneous vascular tumors to large infiltrative lesions.
Definition from the Mondo Disease Ontology (MONDO:0016236), read 2026-09-29. CC BY 4.0.
Features
14 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- Chronic disseminated intravascular coagulationHPOHP:0005520
- Frequent (30% to 79% of cases)
- EdemaHPOHP:0000969
- Frequent (30% to 79% of cases)
- Elevated circulating D-dimer concentrationHPOHP:0033106
- Frequent (30% to 79% of cases)
- Erythematous papuleHPOHP:0030350
- Frequent (30% to 79% of cases)
- Erythematous plaqueHPOHP:0025474
- Frequent (30% to 79% of cases)
- HypofibrinogenemiaHPOHP:0011900
- Frequent (30% to 79% of cases)
- LymphedemaHPOHP:0001004
- Frequent (30% to 79% of cases)
- Microangiopathic hemolytic anemiaHPOHP:0001937
- Frequent (30% to 79% of cases)
- PainHPOHP:0012531
- Frequent (30% to 79% of cases)
- PetechiaeHPOHP:0000967
- Frequent (30% to 79% of cases)
- PurpuraHPOHP:0000979
- Frequent (30% to 79% of cases)
- ThrombocytopeniaHPOHP:0001873
- Frequent (30% to 79% of cases)
Show the remaining 2
- HyperhidrosisHPOHP:0000975
- Occasional (5% to 29% of cases)
- HypertrichosisHPOHP:0000998
- Occasional (5% to 29% of cases)