intravascular large B-cell lymphoma
Findings
No curated finding names intravascular large B-cell lymphoma yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Intravascular large B-cell lymphoma (IVLBCL) is a very rare form of diffuse large B-cell lymphoma characterized by the selective growth of lymphoma cells within the lumina of small blood vessels (especially the capillaries) that most often presents with a wide range of clinical manifestations (as potentially any tissue can be involved), with patients from Western countries more frequently manifesting with neurological and cutaneous symptoms while patients from Asian countries more frequently displaying hepatosplenomegaly and thrombocytopenia. IVLBCL is characterized by an absence of lymphadenopathy, an aggressive clinical course and a poor prognosis.
Definition from the Mondo Disease Ontology (MONDO:0020324), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
Other names
7 names
Resolves to: intravascular large B-cell lymphoma
- Also called
- angioendotheliomatosis proliferans systemisataangiotropic large cell lymphomaangiotropic lymphomaintravascular B-cell lymphomaintravascular lymphomatosismalignant angioendotheliomatosisTappeiner-Pfleger disease