interstitial granulomatous dermatitis with arthritis
Findings
No curated finding names interstitial granulomatous dermatitis with arthritis yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
Interstitial granulomatous dermatitis with arthritis is a rare rheumatologic disease characterized by the occurrence of inflammatory arthritis in association with large, erythematous, symmetrical cutaneous lesions (ranging from typical, but infrequent, cord-like lesions on the flanks to more common violaceous plaques on the trunk and limbs) featuring a typical histologic infiltrate mainly constituted of histiocytes.
Definition from the Mondo Disease Ontology (MONDO:0019199), read 2026-09-29. CC BY 4.0.
Features
8 features
What the disease is reported to present with, and how often among people who have it — never how often a feature means the disease. HPO, annotations 2026-09-02.
- ErythemaHPOHP:0010783
- Obligate (100% of cases)
- Rheumatoid arthritisHPOHP:0001370
- Obligate (100% of cases)
- Elevated circulating C-reactive protein concentrationHPOHP:0011227
- Very frequent (80% to 99% of cases)
- Elevated erythrocyte sedimentation rateHPOHP:0003565
- Very frequent (80% to 99% of cases)
- Inflammatory abnormality of the skinHPOHP:0011123
- Very frequent (80% to 99% of cases)
- PapuleHPOHP:0200034
- Very frequent (80% to 99% of cases)
Where it sits
- A kind of
Other names
2 names
Resolves to: interstitial granulomatous dermatitis with arthritis
- Also called
- Ackerman dermatitis syndromeIGDA