immunotactoid or fibrillary glomerulopathy
Findings
No curated finding names immunotactoid or fibrillary glomerulopathy yet. Everything below is reference data from Mondo, HPO and GenCC, not evidence about what affects it.
Definition
A group of very rare glomerular diseases, composed of immunotactoid glomerulopathy (ITG) and non-amyloid fibrillary glomerulopathy (non-amyloid FGP), that are characterized by mesangial deposition of monoclonal microtubular or polyclonal fibrillar deposits. Both present clinically with nephrotic range proteinuria, hematuria and renal insufficiency leading to renal failure in many cases. ITG is more likely to manifest with underlying lymphoproliferative disease, hypocomplementemia, dysproteinemia, monoclonal gammopathy or occult cryoglobulinemia. Non-amyloid FGP is 10 times more frequent than ITG.
Definition from the Mondo Disease Ontology (MONDO:0019605), read 2026-09-29. CC BY 4.0.
Where it sits
- A kind of
- Narrower terms (2)
Other names
1 name
Resolves to: immunotactoid or fibrillary glomerulopathy
- Also called
- Immunotactoid or fibrillary glomerulonephritis